Malignant Epithelioid Angiomyolipoma of the Kidney (Malignant Perivascular Epithelioid Cell Neoplasm)
نویسندگان
چکیده
منابع مشابه
“Malignant” Perivascular Epithelioid Cell Neoplasm: Risk Stratification and Treatment Strategies
Purpose. Perivascular epithelioid cell tumors (PEComas) are a rare collection of tumors characterized by a myomelanocytic phenotype, and PEComas occurring in "nonclassic" anatomic distributions are known as perivascular epithelioid cell tumor not otherwise specified (PEComa-NOS). This review aims to compile and analyze cases of PEComa-NOS in an effort to better define their natural history. Des...
متن کاملWünderlich syndrome from a malignant epithelioid angiomyolipoma.
Received August 2008 Accepted December 2008 INTRODUCTION Angiomyolipoma of the kidney has classically been considered as a tumor of the connective tissue composed of fat, vascular tissue, and smooth muscle. In most cases, it is a tumor with benign behavior that may appear sporadically or associated with tuberous sclerosis syndrome. Macroscopically, these tumors are greyish yellow in color, and ...
متن کاملMalignant perivascular epithelioid cell tumor of the uterus
Perivascular epithelioid cell tumors (PEComas) are a rare collection of tumors arising in a wide array of anatomic locations and characterized by a myomelanocytic phenotype. PEComas which occur in non-classic anatomic distributions are known as perivascular epithelioid cell tumor-not otherwise specified (PEComa-NOS), and one of the most common primary sites for PEComa-NOS is the uterus. The ris...
متن کاملMalignant perivascular epithelioid cell tumor of the retroperitoneum.
Perivascular epithelioid cell tumors (PEComas) are a rare type of mesenchymal neoplasms characterized by a proliferation of perivascular cells with an epithelioid phenotype and expression of myo-melanocytic markers. The majority of PEComas seem to be benign and usually their prognosis is good. Malignant cases are extremely rare, exhibiting a malignant course with local recurrences and distant m...
متن کاملMalignant Perivascular Epithelioid Cell Tumor of the Esophagus
Malignant perivascular epithelioid cell tumor (PEComa) is a rare tumor composed of hybrid tumor cells characterized by immunoreactivity for both melanocytic and smooth muscle markers. This paper describes the uncommon esophageal location of an 8 cm PEComa in a 75-year-old Caucasian man who was presented with ingravescent dysphagia. Although PEComas arising within the gastrointestinal tract are ...
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ژورنال
عنوان ژورنال: Mayo Clinic Proceedings
سال: 2020
ISSN: 0025-6196
DOI: 10.1016/j.mayocp.2019.11.015